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Case Report

Primary cardiac synovial sarcoma presenting with brain metastases

    Toktam Alirezaei

    Cardiology department of Shohada-e Tajrish Hospital, Shahid Beheshti University of Medical Sciences, Tehran, 1989934148, Iran

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    ,
    Zahra Ansari Aval

    *Author for correspondence: Tel.: +98 212 207 4087;

    E-mail Address: Zahraansariaval@gmail.com

    Cardiovascular Research Center, Shahid Beheshti University of Medical Sciences, Tehran, 1998734383, Iran

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    ,
    Mehrdad Jafari Tadi

    Student Research Committee, School of Medicine, Shahid Beheshti University of Medical Sciences, Tehran, 1985717443, Iran

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    &
    Tahmineh Mollasharifi

    Clinical Research Development Center, Shahid Modarres Educational Hospital, Shahid Beheshti University of Medical Sciences, Tehran, 1998734383, Iran

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    Published Online:14 Jun 2022https://doi.org/10.2217/fca-2022-0002

    Abstract

    Primary cardiac synovial sarcoma is a very rare primary cardiac tumor that usually arises in the right side of the heart. Brain metastases in primary cardiac sarcomas are not uncommon. Because of the wild nature of these tumors, they usually have poor outcomes. This study describes a 29-year-old female who presented with blurred vision, headache, nausea, vomiting and brain lesions in the radiologic study. Incidentally, two-dimensional echocardiography revealed a left atrial lesion. The patient underwent emergency cardiac surgery to resect the left atrial mass that arose from the atrial free wall and pulmonary veins. The diagnosis of the lesion was primary synovial sarcoma in the histopathologic examination.

    Plain language summary

    Tumors that usually arises in the right side of the heart are very rare. These tumors can spread to other parts like brain. Because of the wild nature of these tumors, they usually have poor results. This study describes a 29-year-old female who comes to the hospital with vision problems, headache, nausea, vomiting and brain masses in the imaging. In addition, there was a mass on the left side of her heart. The patient underwent emergency heart surgery to resect the mass that arose from the heart wall and lung veins. The nature of the lesion was primary synovial sarcoma in the pathologic examination.

    Papers of special note have been highlighted as: • of interest; •• of considerable interest

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